Aneuploidy Testing

Aneuploidy Overview

  • 1 in 150 live births: Most common disorders include

    • Trisomy 21 (Down Syndrome): 1 in 800 live births

    • Trisomy 18 (Edward Syndrome): 1 in 7,000 live births

    • 47 XXY (Klinefelter syndrome): 1 in 500 males

    • 45 X (Turner syndrome): 1 in 20,000 females

  • Risk factors: Prior aneuploid fetus, increasing maternal age

  • Testing should be reviewed at first prenatal visit

Screening Options

  • First Trimester Combined Screen: 11+0 to 13+6 WGA

    • Screens for trisomy 21 only (85% detection rate)

    • Measurements/labs include

      • Nuchal translucency measurement (sonographer skill dependent)

      • Serum free beta-hCG

      • Total H-hCG

      • Pregnancy associated plasma protein A analyte (PAPP-A) levels

  • Quadruple Screen (AFP Tetra): 15+0 to 22+6 WGA

    • Screens for trisomy 21 (80% detection rate), trisomy 18, and open fetal defects

    • Labs include

      • Serum free beta-hCG

      • Inhibin A (placental protein)

      • Unconjugated estriol (uE3 - dominant estrogen produced during pregnancy)

      • Alpha fetoprotein (AFP - produced by developing liver and yolk sac)

  • Cell free DNA: 10+0 WGA to term

    • Information provided

      • All options tests for trisomy 21 (98% detection), trisomy 18, and trisomy 13, fetal sex

      • Additional information depends on the specific panel selected

    • Most commonly used in patients with advanced maternal age, i.e. > 35 years old at time of delivery

    • Verify insurance coverage before sending test

Sequential Screening Method

  • Stepwise model: Perform first trimester combined screen

    • Positive result → perform cfDNA or diagnostic testing

    • Negative result → perform Quad screen

  • Contingent model: Perform first trimester combined screen

    • High risk → perform cfDNA or chorionic villus sampling

    • Intermediate risk → perform Quad screen

    • Low risk→ no further screening

Positive Screens

  • Educate family about condition

  • Discussion options, e.g. referral to genetics for further counseling, pregnancy termination, referral to a tertiary care center, perinatal hospice, adoption, etc.

More information: See ACOG Bulletin 163